(3) Progressive difficulty in speaking and swallowing, speech may be nasal
Mental facilities are not affected.
Death usually occurs 3-5 years after onset.
c. Medical and Nursing Management
Objective--to support the patient and improve quality of life.
(2) Instruct the patient to perform active exercises and range of motion
exercises to strengthen uninvolved muscles and prevent disuse atrophy.
Utilize braces, splints, canes, etc., to keep patient mobile as long as
Assist the patient to prevent complications that may result from
(a) Keep suction apparatus at bedside, as aspiration is a constant
(b) Instruct patient to drink and eat in an upright position with the neck
Use soft cervical collar if patient has difficulty holding head up.
(d) Give semi-soft foods. Avoid easily-aspirated pureed foods and
mucous producing foods (milk).
(e) Keep in mind that patient may have frequent outbursts of laughing
Develop communication system when speech is lost.
Give patient and family compassionate and caring support.
(a) Allow expressions of feelings and frustrations about losses and